Bentall Procedure for an Adolescent with Sickle Cell Disease, Hodgkin’s Lymphoma, and old Cerebrovascular Accident

Cardiopulmonary bypass (CPB) in patients with sickle cell anemia can trigger lethal vaso-occlusive crises, especially cases of hypoxia, hypothermia, acidosis, or low-flow states. We described a patient who had bicuspid aortic valve stenosis and aneurysmal dilatation the ascending aorta complicated infective endocarditis. The history stroke. During routine workup, Hodgkin’s Lymphoma was diagnosed. underwent exchange transfusion preoperatively immediately before initiation CPB. performed Bentall procedure, discharged stable condition. Sickle Cell Disease be very challenging during CPB, special precautions are required to prevent crises.